XMTVI Maxamum Metabolic Formula

XMTVI Maxamum is a medical food formulated for the dietary management of vitamin B12-unresponsive methylmalonic acidemia (MMA) and propionic acidemia (PA) — inherited metabolic disorders in which the body cannot properly break down certain amino acids. These conditions require strict, lifelong nutritional control, and this formula is built to support that need in older children, teens, and adults who have outgrown lower-calorie infant and pediatric versions.

The "Maxamum" designation reflects its higher protein-equivalent and energy density, intended for individuals with greater nutritional demands. It provides protein free of isoleucine, methionine, threonine, and valine — the amino acids that must be limited in MMA and PA — while delivering the remaining essential amino acids, vitamins, minerals, and trace elements needed to support normal growth and metabolic stability. Natural protein from food is then added separately under the guidance of a metabolic dietitian to meet each person's individual tolerance.

Because dosing, natural-protein allowances, and formula selection are highly individualized, XMTVI Maxamum should only be used under the supervision of a physician or metabolic specialist familiar with the patient's care plan. Families managing these disorders often coordinate multiple formulas as needs change with age, growth, and lab results.

If you are managing a related inherited metabolic condition, you may also be looking at XMet Maxamum for methionine restriction, XLeu Maxamum for leucine-related disorders, or XPhe Maxamum for phenylketonuria (PKU). Each is tailored to a specific amino acid restriction, so confirm the correct formula with your care team before ordering.